Peripapillary pachychoroid syndrome: a case report
Author: Sofia Anagnostopoulou (Greece)
Co-authors: Maria Sourla, Paraskevi Karra, Vassiliki Dimera, Eleni Spathi
To report a case of a Peripapillary Pachychoroid Syndrome in an asymptomatic patient, which is characterized by a relatively thickened nasal macular choroid with associated intraretinal and subretinal fluid in the nasal macular region extending from the disc margin.
Ophthalmology Department, General Hospital of Larissa, Larissa, Greece
This is a case report of an 80-year-old male patient who visited our Department for a routine examination. We performed classic ophthalmic evaluation and used Optical Coherence Tomography (OCT), Enhanced Depth Imaging OCT (EDI-OCT), Fluorescein Angiography (FA), Fundus Autofluorescence Imaging (FAF) and Optical Coherence Tomography Angiography (OCTA) to evaluate the case.
Best corrected visual acuity (BCVA) was 9/10 in both eyes and Amsler test was positive in his left eye. Slit lamp examination was normal. Fundoscopy revealed perimacular retinal pigment epithelium (RPE) alterations of the right eye and peripapillary hyperpigmentation in the left eye. OCT of the left eye illustrated intraretinal fluid both on the temporal side and, to a lesser extent, on the nasal side of the left optic disc. EDI-OCT measurements of the choroidal thickness were 810μm under the macula of the right eye and 755μm nasally to the left macula indicating a thickened choroid. FA showed no leakage in both eyes and mottled fluorescence in the aforementioned hyperpigmented areas. FAF illustrated mottled autofluorescence of the RPE in the left peripapillary region. OCTA revealed no signs of neovasculopathy in both eyes.
We described a typical case of Peripapillary Pachychoroid Syndrome (PPS) which was recently described as an entity of the pachychoroid disease spectrum. The condition may share features with other pachychoroid entities and, therefore, patients with PPS should be monitored routinely.
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